Abstract

 

Tuberous sclerosis known as Epiloia and Bourneville’s disease is a neurocutane syndrome, which is resulted from the programmed hyperplasia of ectodermal and mesodermal cells. The term tuberous sclerosis complex is now widely used. The term of the complex remarks variable multisystemic involvement and genetic heterogeneity of the disease. The disease showing different variations from the age of onset and the severity have classical triads ofepilepsy, mental retardation and adenoma sebaceum. The management of the disease is made according to the affected organ.

This rarely seen disease was discussed because of the two different cases admitted to our clinics and detailed information about the cutaneous findings are given.

Key Word: Tuberous sclerosis, Adenoma sebaceum, Koenen tumor